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Advance Research Journal of Cancer
[ ISSN : 2833-3543 ]


Malignant Hemangiopericytoma in Thigh: A Case Report and Literature Review

Research Article
Volume 1 - Issue 1


Amani Saleh Hadi, Rafaat Al Areqee and SadikSaif Mohammed Aklan

Published : May 07, 2020

Abstract

Hemangiopericytoma (HPC) is an uncommon soft tissue sarcoma of vascular origin. It can develop anywhere there are capillaries; hence, it causes many unique problems of diagnosis and therapy. It occurs more frequently in the extremities than elsewhere in the body although it can arise in any organ. The tumour may develop over period of months and even years and in patients of all ages equally in men and women. The most critical aspect of treatment is an accurate histological diagnosis separating it from other angiosarcomas and benign tumours of blood vessels such as the solitary glomus tumour. Wide surgical excision is mainstay of treatment. However, adjuvant radiotherapy and chemotherapy are desirable because the malignant nature of this tumour is frequently unpredictable. Adjuvant therapy recommended for metastases, recurrence and incomplete resection long term fellow up is essential in all cases as recurrence can occur several years after treatment. Where little or no experience with managing this tumour exists is important to beware of its clinical behaviour and the treatment options hence this case report. We present unusual case of histologically confirmed malignant hemangiopericytoma of left thigh in 70-year female with metastasis to lungs with review of literature, to demonstrate the malignant character of this neoplasm and its variable prognosis.