Gorlin–Goltz syndrome, or nevoid basal cell carcinoma syndrome, is an uncommon autosomal dominant disorder characterized by multiple odontogenic keratocysts, basal cell carcinomas, and a spectrum of skeletal and developmental anomalies. We present the case of a 13-year-old male who reported with progressive mandibular swellings and facial asymmetry. Clinical examination and panoramic radiography revealed multiple well-circumscribed radiolucent lesions involving both jaws, consistent with odontogenic keratocysts. The diagnosis was established based on clinic-radiological f indings and confirmed histo-pathologically. Surgical enucleation of the cysts was performed with adjunctive measures to reduce the risk of recurrence. This case underscores the importance of early recognition of Gorlin–Goltz syndrome in paediatric patients, the necessity of multidisciplinary management, and the imperative for long term surveillance to mitigate morbidity and detect associated systemic manifestations.